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ACG Case Reports Journal

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lesions.","https://images.journals.lww.com/acgcr/Rollover.02075970-202410000-00019.F1.jpeg","https://images.journals.lww.com/acgcr/Gallery.02075970-202410000-00019.F1.jpeg","https://journals.lww.com/acgcr/_layouts/oaks.journals/ImageView.aspx?k=acgcr:2024:10000:00019&i=F1&year=2024&issue=10000&article=00019&type=Fulltext","https://images.journals.lww.com/acgcr/Original.02075970-202410000-00019.F1.jpeg","/acgcr/pages/imagegallery.aspx?year=2024&issue=10000&article=00019", "acgcr_2024_10000_00019_F1");images["F2"]=new image("F2","F3","F1","Figure 2.","Positron emission tomography-computed tomography scan showed fluorodeoxyglucose uptake in the liver, spleen, and bone 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Infiltrative Case of Angiosarcoma Causing Portal Hypertension', '10102024', 'Gina Bae, Katie A. Dunleavy, Catherine Hagen, et al', '11', '10', '\u00A9 2024 The Author(s). Published by Wolters Kluwer Health, Inc. on behalf of The American College of Gastroenterology.', '02075970-202410000-00019', '', true, 'CCBY-NC-ND'); } </script> <div id="ArticleContainer"> <article id="ej-article-view" class="js-article-view ej-article-view" xmlns:ssr="http://ssr-eus-go-csi.cloudapp.net/v1/assets" xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xhtml="http://www.w3.org/1999/xhtml"><section class="ejp-r-article-subsection"><div class="ejp-r-article-subsection__text">CASE REPORT: LIVER</div></section><header class="ejp-article-header"><h1 class="ejp-article-title">An Infiltrative Case of Angiosarcoma Causing Portal Hypertension</h1></header><section id="ejp-article-authors"><p id="P7">Bae, Gina BS<sup xmlns:mrws="http://webservices.ovid.com/mrws/1.0">1</sup>; Dunleavy, Katie A. MB, BCh, BAO<sup xmlns:mrws="http://webservices.ovid.com/mrws/1.0">2</sup>; Hagen, Catherine MD<sup xmlns:mrws="http://webservices.ovid.com/mrws/1.0">3</sup>; Simonetto, Douglas A. MD<sup xmlns:mrws="http://webservices.ovid.com/mrws/1.0">2</sup>; Abdelmalek, Manal F. MD<sup xmlns:mrws="http://webservices.ovid.com/mrws/1.0">2</sup></p><section><a href="#" id="ejp-article-authors-link"> Author Information <i class="wk-icon-arrow-down-r"></i></a></section></section><section id="ejp-article-authors-info" class="ejp-article-authors-info ejp-article-authors-info--hidden"><div class="ejp-article-authors-info-holder"> <p id=""><sup xmlns:mrws="http://webservices.ovid.com/mrws/1.0">1</sup>Alabama College of Osteopathic Medicine, Dothan, AL</p> <p id=""><sup xmlns:mrws="http://webservices.ovid.com/mrws/1.0">2</sup>Division of Gastroenterology and Hepatology, Mayo Clinic College of Medicine, Rochester, MN</p> <p id=""><sup xmlns:mrws="http://webservices.ovid.com/mrws/1.0">3</sup>Department of Laboratory Medicine and Pathology, Mayo Clinic College of Medicine, Rochester, MN</p> <p id="cor1"><strong xmlns:mrws="http://webservices.ovid.com/mrws/1.0">Correspondence:</strong> Katie A. Dunleavy, MB, BCh, BAO (<span><a href="/cdn-cgi/l/email-protection#bfd2ded6d3cbd085fbcad1d3dadec9c691d4decbd6daffd2dec6d091dadbca" onclick="javascript:window.open('mailto:mailto:Dunleavy.katie@mayo.edu');return false"><span class="__cf_email__" data-cfemail="783c0d16141d190e015613190c111d3815190117561d1c0d">[email&#160;protected]</span></a></span>).</p> <p id="">This is an open access article distributed under the terms of the <span><a href="http://creativecommons.org/licenses/by-nc-nd/4.0/" onclick="javascript:window.open('http://creativecommons.org/licenses/by-nc-nd/4.0/');return false">Creative Commons Attribution-Non Commercial-No Derivatives License 4.0 (CCBY-NC-ND)</a></span>, where it is permissible to download and share the work provided it is properly cited. The work cannot be changed in any way or used commercially without permission from the journal.</p> </div></section><section id="article-journal-info"><div class="ej-journal-info"><span class="ej-journal-name">ACG Case Reports Journal </span><span id="ej-journal-date-volume-issue-pg"><a href="/acgcr/toc/2024/10000">11(10):p e01532, October 2024.</a></span><span> | </span><span class="ej-journal-doi">DOI: </span>10.14309/crj.0000000000001532<a id="ej-article-indicators-ccl" onmouseover="javascript:Tooltip_CCL('This is an open access article distributed under the terms of the Creative Commons Attribution-Non Commercial-No Derivatives License 4.0 (CCBY-NC-ND), where it is permissible to download and share the work provided it is properly cited. The work cannot be changed in any way or used commercially without permission from the journal.')" onmouseout="javascript:Tooltip_MouseOut()" href="http://creativecommons.org/licenses/by-nc-nd/4.0/" target="_blank"><span class="ejp-article-indicators__ccl"></span></a></div></section><section id="ejp-article-indicators" class="ejp-article-indicators"><ul class="ejp-article-indicators__list"> <li id="ej-article-indicators-open" class="ejp-article-indicators__list-item" onmouseover="javascript:Tooltip_Open()" onmouseout="javascript:Tooltip_MouseOut()"><span class="ejp-indicator">Open</span></li> </ul><button id="openArticleMetricsPopupButton" type="button" class="wk-button wk-button-ghost wk-button-icon-left ejp-article-metrics-btn" data-articleMetricsEndpoint="//services.journals.lww.com/IntegrationServices/ArticleMetricsService.svc" data-articleMetricsDetailsUrl="https://wolterskluwer.altmetric.com/details/" data-doi="10.14309/crj.0000000000001532" data-suiteId="vrs_woltere_journalsglobalvrs" data-articlePublicationDate="2024-10-10" data-articlePublicationDateString="October 10, 2024" data-receivedDate="2024-02-05" data-revisionReceivedDate="" data-acceptedDate="2024-09-09" data-crossrefRefLinkRoot="https://doi.org/" data-medlineRefLinkRoot="http://www.ncbi.nlm.nih.gov/pubmed/" data-pubMedId="39391806"><i class="wk-icon-filled-chart-r"></i><i class="wk-icon-filled-chart-white-r"></i> Metrics </button></section><section class="ejp-article-tabs" id="abstractWrap"><h2 class="ejp-article-tabs-heading">Abstract</h2> <div class="ejp-article-tabs__tabpanel" id="panel1" role="tabpanel" aria-labelledby="tab1"> <div id="article-abstract-content1"> <div class="ejp-article-text-abstract"> <p>Hepatic angiosarcoma is a rare and aggressive liver tumor. We report a case study of an 82-year-old elderly gentleman who presented with failure to thrive and ascites. Initially suspected to be cirrhosis, biopsy results eventually concluded angiosarcoma of the liver. Our patient presented with an infiltrative form, rather than distinct masses, which led to portal hypertension and ascites. The variance in symptomatology and radiology presentations make a diagnosis of hepatic angiosarcoma challenging and require a high index of suspicion.</p> </div> </div> </div></section><div class="ejp-fulltext-content js-ejp-fulltext-content"><section id="ArticleBody"><h2 class="ejp-article-outline-heading" data-level="1" id="s1">INTRODUCTION</h2> <p id="JCL-P-1">Hepatic angiosarcoma (HAS) is a rare and aggressive malignancy, accounting for only 2% of primary liver malignancy with majority of untreated patients dying within 6 months.<sup xmlns:mrws="http://webservices.ovid.com/mrws/1.0"><sup><a class="ejp-citation-link js-ejp-citation-link" data-reference-links="R1 R2">1,2</a></sup></sup> A review of the National Cancer Institute's epidemiology database identified only 207 patients with primary HAS over a period of 30+ years.<sup xmlns:mrws="http://webservices.ovid.com/mrws/1.0"><sup><a class="ejp-citation-link js-ejp-citation-link" data-reference-links="R3">3</a></sup></sup> Certain exposure agents—such as vinyl chloride, Thorotrast, arsenic, and anabolic steroid use—have been linked with HAS, although 75% of etiology still remains unknown.<sup xmlns:mrws="http://webservices.ovid.com/mrws/1.0"><sup><a class="ejp-citation-link js-ejp-citation-link" data-reference-links="R4 R5">4,5</a></sup></sup> The largely idiopathic nature, low incidence rate, and variable presentation hinder the development of efficient diagnostic protocols and effective treatment options. Here, we present a case of an infiltrative presentation of this exceedingly rare disease.</p> <h2 class="ejp-article-outline-heading" data-level="1" id="s2">CASE REPORT</h2> <p id="JCL-P-2">An 82-year-old man was admitted for failure to thrive. He had large ascites and splenomegaly. Laboratory workup revealed thrombocytopenia, aspartate aminotransferase 166 U/L, alanine aminotransferase 60 U/L, total bilirubin 2.8 mg/dL, and alkaline phosphatase 500 U/L. Albumin was 3.4 g/dL. Serum ascites albumin gradient &gt;1.1 suggested ascites secondary to portal hypertension. The total protein of the ascitic fluid was 1.0 g/dL with negative cytology. Abdominal computed tomography demonstrated splenic lesions (<a href="javascript:void(0)" onclick="javascript:showSlideShowByImageID('F1', '02075970-202410000-00019');">Figure 1</a>). Owing to concern for infectious etiology, the inpatient medical team ordered serology for Coxiella, Bartonella, and Brucellosis, all of which were negative. Positron emission tomography-computed tomography scan showed fluorodeoxyglucose uptake in the liver, spleen, and bone marrow (<a href="javascript:void(0)" onclick="javascript:showSlideShowByImageID('F2', '02075970-202410000-00019');">Figure 2</a>). Flow cytometry and bone marrow aspirates were unrevealing. A detailed history and physical examination did not provide further concerns for alcohol-associated liver disease, metabolic-associated liver disease, or drug-induced liver injury. Chronic hepatitis A, B, and D were negative. Genetic causes including α-1 antitrypsin deficiency and hereditary hemochromatosis were excluded. No features of autoimmune liver disease were found on liver biopsy. Imaging did not show concern for chronic Budd-Chiari syndrome. Liver biopsy was diagnostic for HAS (<a href="javascript:void(0)" onclick="javascript:showSlideShowByImageID('F3', '02075970-202410000-00019');">Figures 3 and 4</a>: Hematoxylin and eosin stain, magnification, 200×; immunohistochemical stain for ERG showing nuclear tumor positivity, magnification 200×), with atypical spindle cell proliferation, hyperchromatic nuclei, and scant pale eosinophilic cytoplasm growing along sinusoids causing destruction of liver cell plates. Detailed medical and surgical history following the diagnosis did not elucidate clear underlying risk of development of this liver tumor. Owing to our patient's age and comorbidities, his family elected to transition him to comfort care. He died a few weeks later.</p><section class="ejp-r-article-images"><figure class="ejp-r-article-images__figure"><a href="javascript:void(0)" class="ejp-r-article-images__image-link" onclick="showSlideShowByImageID('F1', '02075970-202410000-00019')"><img class="ejp-r-article-images__img js-lazy-load lazy-load" src="javascript:void(0);" data-src="https://images.journals.lww.com/acgcr/ArticleViewerPreview.02075970-202410000-00019.F1.jpeg" data-srcset="https://images.journals.lww.com/acgcr/ArticleViewerPreview@2.02075970-202410000-00019.F1.jpeg 2x" srcset="" alt="F1"></a><figcaption class="ejp-r-article-images__figcaption"><a href="javascript:void(0)" class="ejp-r-article-images__figcaption-link" onclick="showSlideShowByImageID('F1', '02075970-202410000-00019')">Figure 1.: </a><div class="ejp-r-article-images__figcaption-text">Abdominal computed tomography demonstrating splenic lesions.</div></figcaption></figure><figure class="ejp-r-article-images__figure"><a href="javascript:void(0)" class="ejp-r-article-images__image-link" onclick="showSlideShowByImageID('F2', '02075970-202410000-00019')"><img class="ejp-r-article-images__img js-lazy-load lazy-load" src="javascript:void(0);" data-src="https://images.journals.lww.com/acgcr/ArticleViewerPreview.02075970-202410000-00019.F2.jpeg" data-srcset="https://images.journals.lww.com/acgcr/ArticleViewerPreview@2.02075970-202410000-00019.F2.jpeg 2x" srcset="" alt="F2"></a><figcaption class="ejp-r-article-images__figcaption"><a href="javascript:void(0)" class="ejp-r-article-images__figcaption-link" onclick="showSlideShowByImageID('F2', '02075970-202410000-00019')">Figure 2.: </a><div class="ejp-r-article-images__figcaption-text">Positron emission tomography-computed tomography scan showed fluorodeoxyglucose uptake in the liver, spleen, and bone marrow.</div></figcaption></figure><figure class="ejp-r-article-images__figure"><a href="javascript:void(0)" class="ejp-r-article-images__image-link" onclick="showSlideShowByImageID('F3', '02075970-202410000-00019')"><img class="ejp-r-article-images__img js-lazy-load lazy-load" src="javascript:void(0);" data-src="https://images.journals.lww.com/acgcr/ArticleViewerPreview.02075970-202410000-00019.F3.jpeg" data-srcset="https://images.journals.lww.com/acgcr/ArticleViewerPreview@2.02075970-202410000-00019.F3.jpeg 2x" srcset="" alt="F3"></a><figcaption class="ejp-r-article-images__figcaption"><a href="javascript:void(0)" class="ejp-r-article-images__figcaption-link" onclick="showSlideShowByImageID('F3', '02075970-202410000-00019')">Figure 3.: </a><div class="ejp-r-article-images__figcaption-text">Liver biopsy was diagnostic for hepatic angiosarcoma (Hematoxylin and eosin stain; magnification, 200×) with atypical spindle cell proliferation, hyperchromatic nuclei, and scant pale eosinophilic cytoplasm growing along sinusoids causing destruction of liver cell plates.</div></figcaption></figure><figure class="ejp-r-article-images__figure"><a href="javascript:void(0)" class="ejp-r-article-images__image-link" onclick="showSlideShowByImageID('F4', '02075970-202410000-00019')"><img class="ejp-r-article-images__img js-lazy-load lazy-load" src="javascript:void(0);" data-src="https://images.journals.lww.com/acgcr/ArticleViewerPreview.02075970-202410000-00019.F4.jpeg" data-srcset="https://images.journals.lww.com/acgcr/ArticleViewerPreview@2.02075970-202410000-00019.F4.jpeg 2x" srcset="" alt="F4"></a><figcaption class="ejp-r-article-images__figcaption"><a href="javascript:void(0)" class="ejp-r-article-images__figcaption-link" onclick="showSlideShowByImageID('F4', '02075970-202410000-00019')">Figure 4.: </a><div class="ejp-r-article-images__figcaption-text">Liver biopsy was diagnostic for hepatic angiosarcoma (immunohistochemical stain for ERG showing nuclear tumor positivity; magnification, 200×) with atypical spindle cell proliferation, hyperchromatic nuclei, and scant pale eosinophilic cytoplasm growing along sinusoids causing destruction of liver cell plates.</div></figcaption></figure></section><h2 class="ejp-article-outline-heading" data-level="1" id="s3">DISCUSSION</h2> <p id="JCL-P-3">HAS is a rare malignant tumor which arises from vascular endothelium with poor prognosis and rapid clinical decline.<sup xmlns:mrws="http://webservices.ovid.com/mrws/1.0"><sup><a class="ejp-citation-link js-ejp-citation-link" data-reference-links="R6">6</a></sup></sup> Clinical presentation can be nonspecific with hepatomegaly, pain, anorexia, fatigue, and weight loss. Most cases present as hypervascular foci, allowing for detection as distinct masses through contrast imaging.<sup xmlns:mrws="http://webservices.ovid.com/mrws/1.0"><sup><a class="ejp-citation-link js-ejp-citation-link" data-reference-links="R7">7</a></sup></sup> This patient presented with an infiltrative form, highlighting the difficulty with early diagnosis due to the variance in symptomatology and radiologic features. Moreover, extrahepatic involvement is common, and, in this case, the splenic lesions found on the CT scan may present as metastasis. Interestingly, this patient also presented with features of noncirrhotic portal hypertension. A study by Wu X et al suggested that HAS and noncirrhotic portal hypertension may share similar etiologies although no clear associations have been made yet.<sup xmlns:mrws="http://webservices.ovid.com/mrws/1.0"><sup><a class="ejp-citation-link js-ejp-citation-link" data-reference-links="R8">8</a></sup></sup></p> <p id="JCL-P-4">The number of patients with primary HAS is low, and furthermore, the proportion of those with the infiltrative form is even more rare. Primary angiosarcoma of the liver disproportionately occur in men with peak incidence in the sixth or seventh decade of life.<sup xmlns:mrws="http://webservices.ovid.com/mrws/1.0"><sup><a class="ejp-citation-link js-ejp-citation-link" data-reference-links="R5">5</a></sup></sup> Unfortunately, prognosis is poor with a rapid clinical decline 6–12 months following diagnosis. Complications include hepatic failure or intra-abdominal bleeding secondary to rupture. The poor prognosis is mostly attributed to the aggressive nature of the tumor, early metastasis, and the relatively low awareness among physicians, which further delay the diagnostic process and optimal treatment administration.<sup xmlns:mrws="http://webservices.ovid.com/mrws/1.0"><sup><a class="ejp-citation-link js-ejp-citation-link" data-reference-links="R9">9</a></sup></sup> Currently, there are no established guidelines for management and treatment. In patients with good functional status, radical resection can be considered. Liver transplantation is contraindicated due to high rate of recurrence. Transcatheter arterial chemoembolization can be used to control bleeding or to palliate a dominant mass.</p> <p id="JCL-P-5">This case presented a diagnostic challenge because our patients' workup for failure to thrive initially revealed anemia, thrombocytopenia, elevated liver biochemistries, and splenic lesions. He was found to have an infiltrative form of HAS, rather than distinct masses, which may have contributed to the portal hypertension and ascites. Without the presence of the splenic lesions, it is likely he would have been diagnosed with cirrhosis. As infiltrative angiosarcoma is a rare finding on workup for liver disease, this case helps highlight keeping the differential diagnosis broad as you evaluate for nonspecific symptoms of pain, fatigue, and weight loss in the setting of hepatomegaly.</p> <h2 class="ejp-article-outline-heading" data-level="1" id="s4">DISCLOSURES</h2> <p id="JCL-P-6">Author contributions: G. Bae and KA Dunleavy wrote and revised the manuscript. C. Hagen provided the radiographic and histologic images. DA Simonetto and MF Abdelmalek supervised and reviewed the manuscript for intellectual content. KA Dunleavy is the article guarantor.</p> <p id="JCL-P-7">Financial disclosure: None to report.</p> <p id="JCL-P-8">Informed consent was obtained for this report.</p></section><section id="article-references" class="article-references js-article-references"><h2 class="ejp-article-outline-heading" data-level="1" id="JCL-L-0">REFERENCES</h2> <div id="R1" class="article-references__item js-article-reference">1. Chaudhary P, Bhadana U, Singh RA, Ahuja A. Primary hepatic angiosarcoma. 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BMJ Case Rep. 2018;2018:bcr2018225896.<div> <ul class="article-references__item-links"> <li class="internal-links"><a href="#JCL-P-3"> Cited Here</a> | </li> <li><a href="https://scholar.google.com/scholar_lookup?title=Hepatic+angiosarcoma+as+a+cause+of+acute+liver+failure&amp;publication_year=2018&amp;author=G+Singh&amp;author=C+Mills&amp;author=K+Asadi&amp;author=A+Testro" onclick="javascript:window.open('https://scholar.google.com/scholar_lookup?title=Hepatic+angiosarcoma+as+a+cause+of+acute+liver+failure&amp;publication_year=2018&amp;author=G+Singh&amp;author=C+Mills&amp;author=K+Asadi&amp;author=A+Testro');return false">Google Scholar</a></li> </ul> </div> </div> <div id="R7" class="article-references__item js-article-reference">7. Pickhardt PJ, Kitchin D, Lubner MG, Ganeshan DM, Bhalla S, Covey AM. Primary hepatic angiosarcoma: Multi-institutional comprehensive cancer centre review of multiphasic CT and MR imaging in 35 patients. Eur Radiol. 2015;25(2):315–22.<div> <ul class="article-references__item-links"> <li class="internal-links"><a href="#JCL-P-3"> Cited Here</a> | </li> <li><a href="https://scholar.google.com/scholar_lookup?title=Primary+hepatic+angiosarcoma%3a+Multi-institutional+comprehensive+cancer+centre+review+of+multiphasic+CT+and+MR+imaging+in+35+patients&amp;publication_year=2015&amp;author=PJ+Pickhardt&amp;author=D+Kitchin&amp;author=MG+Lubner&amp;author=DM+Ganeshan&amp;author=S+Bhalla&amp;author=AM+Covey" onclick="javascript:window.open('https://scholar.google.com/scholar_lookup?title=Primary+hepatic+angiosarcoma%3a+Multi-institutional+comprehensive+cancer+centre+review+of+multiphasic+CT+and+MR+imaging+in+35+patients&amp;publication_year=2015&amp;author=PJ+Pickhardt&amp;author=D+Kitchin&amp;author=MG+Lubner&amp;author=DM+Ganeshan&amp;author=S+Bhalla&amp;author=AM+Covey');return false">Google Scholar</a></li> </ul> </div> </div> <div id="R8" class="article-references__item js-article-reference">8. Wu X, Yu X, Gan Q, et al. Primary hepatic angiosarcoma with noncirrhotic portal hypertension: A case report. Front Oncol. 2023;13:1037820.<div> <ul class="article-references__item-links"> <li class="internal-links"><a href="#JCL-P-3"> Cited Here</a> | </li> <li><a href="https://scholar.google.com/scholar_lookup?title=Primary+hepatic+angiosarcoma+with+noncirrhotic+portal+hypertension%3a+A+case+report&amp;publication_year=2023&amp;author=X+Wu&amp;author=X+Yu&amp;author=Q+Gan" onclick="javascript:window.open('https://scholar.google.com/scholar_lookup?title=Primary+hepatic+angiosarcoma+with+noncirrhotic+portal+hypertension%3a+A+case+report&amp;publication_year=2023&amp;author=X+Wu&amp;author=X+Yu&amp;author=Q+Gan');return false">Google Scholar</a></li> </ul> </div> </div> <div id="R9" class="article-references__item js-article-reference">9. Lin XJ, Luo HC. Rare infiltrative primary hepatic angiosarcoma: A case report and review of literature. World J Gastrointest Oncol. 2024;16(7):3341–9.<div> <ul class="article-references__item-links"> <li class="internal-links"><a href="#JCL-P-4"> Cited Here</a> | </li> <li><a href="https://scholar.google.com/scholar_lookup?title=Rare+infiltrative+primary+hepatic+angiosarcoma%3a+A+case+report+and+review+of+literature&amp;publication_year=2024&amp;author=XJ+Lin&amp;author=HC+Luo" onclick="javascript:window.open('https://scholar.google.com/scholar_lookup?title=Rare+infiltrative+primary+hepatic+angiosarcoma%3a+A+case+report+and+review+of+literature&amp;publication_year=2024&amp;author=XJ+Lin&amp;author=HC+Luo');return false">Google Scholar</a></li> </ul> </div> </div> <div class="article-references__button-container"></div></section><div><strong>Keywords:</strong><p id="">hepatic angiosarcoma; hepatic tumor; portal hypertension</p> </div><section class="ej-article-copyright">© 2024 The Author(s). 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