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andiquest;En quandeacute; punto nos encontramos en el tratam | 1100356
<!doctype html> <html lang="es"> <head> <title>andiquest;En quandeacute; punto nos encontramos en el tratam | 1100356</title> <meta name="keywords" content="Karin Del Vecchio*, Alice Pozza, Giovanni Di Salvo , "/> <meta name="description" content="La miocardiopatía hipertrófica pediátrica (MCH) tiene una amplia gama de manifestaciones clínicas. La obstrucción del tr..1100356"/> <meta name="citation_publisher" content="Longdom Publicaci贸n SL" /> <meta name="citation_journal_title" content="Cardiolog铆a Cl铆nica y Experimental"> <meta name="citation_title" content="andiquest;En quandeacute; punto nos encontramos en el tratamiento de la miocardiopatandiacute;a hipertrandoacute;fica en niandntilde;os? El papel de la disopiramida y nuevos medicamentos en el horizonte "> <meta name="citation_author" content="Karin Del Vecchio" /> <meta name="citation_author" content="Alice Pozza" /> <meta name="citation_author" content="Giovanni Di Salvo" /> <meta name="citation_year" content=""> <meta name="citation_volume" content="15"> <meta name="citation_issue" content="10"> <meta name="citation_abstract" content="La miocardiopatía hipertrófica pediátrica (MCH) tiene una amplia gama de manifestaciones clínicas. La obstrucción del tracto de salida del ventrículo izquierdo (OTVI) en reposo está presente en hasta un tercio de los niños con MCH, y un 50%-60% adicional de los niños sintomáticos desarrolla un gradiente con el esfuerzo. Las opciones de tratamiento son limitadas y hay una relativa falta de datos sobre la población pediátrica. La disopiramida es un bloqueador de los canales de sodio con propiedades inotrópicas negativas. Esta terapia reduce eficazmente la OTVVI en adultos con MCH y retrasa las intervenciones quirúrgicas, pero no está autorizado para su uso en niños. Este estudio tuvo como objetivo revisar y analizar la influencia de la disopiramida sobre las características fisiopatológicas, clínicas, electrocardiográficas y ecocardiográficas de los pacientes con MCH en la infancia, la niñez, la adolescencia y la edad adulta. Si bien la disopiramida sigue siendo una base en el tratamiento de la MCH pediátrica, la llegada de mavacamten y aficamten anuncia una nueva era de posibles avances. Estas terapias emergentes podrían mejorar significativamente la calidad de vida y el pronóstico de los pacientes jóvenes con miocardiopatía hipertrófica. 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title="haga clic aqu铆">Qu铆mica</a><br> </nav> </div> </div> <!--===========open access journals=================--> </aside> <div class="col-12 col-sm-9"> <h2 class="heading-1">abstracto</h2> <h3 class="">¿En qué punto nos encontramos en el tratamiento de la miocardiopatía hipertrófica en niños? El papel de la disopiramida y nuevos medicamentos en el horizonte </h3> <p> <i class="fas fa-user"></i> Karin Del Vecchio*, Alice Pozza, Giovanni Di Salvo </p> <p>La miocardiopatía hipertrófica pediátrica (MCH) tiene una amplia gama de manifestaciones clínicas. La obstrucción del tracto de salida del ventrículo izquierdo (OTVI) en reposo está presente en hasta un tercio de los niños con MCH, y un 50%-60% adicional de los niños sintomáticos desarrolla un gradiente con el esfuerzo. Las opciones de tratamiento son limitadas y hay una relativa falta de datos sobre la población pediátrica. La disopiramida es un bloqueador de los canales de sodio con propiedades inotrópicas negativas. Esta terapia reduce eficazmente la OTVVI en adultos con MCH y retrasa las intervenciones quirúrgicas, pero no está autorizado para su uso en niños. Este estudio tuvo como objetivo revisar y analizar la influencia de la disopiramida sobre las características fisiopatológicas, clínicas, electrocardiográficas y ecocardiográficas de los pacientes con MCH en la infancia, la niñez, la adolescencia y la edad adulta. Si bien la disopiramida sigue siendo una base en el tratamiento de la MCH pediátrica, la llegada de mavacamten y aficamten anuncia una nueva era de posibles avances. Estas terapias emergentes podrían mejorar significativamente la calidad de vida y el pronóstico de los pacientes jóvenes con miocardiopatía hipertrófica.</p> <div class="alert alert-info text-left"><b>Descargo de responsabilidad:</b> este resumen se tradujo utilizando herramientas de inteligencia artificial y a煤n no ha sido revisado ni verificado.</div> <div class="nav social-icons"> <a class="nav-link w-auto">Comparte este art铆culo</a> <a title="haga clic aqu铆" target="_blank" href="https://www.facebook.com/sharer.php?u=https://spanish.longdom.org/abstract/where-do-we-stand-in-the-treatment-of-hcm-in-children-the-role-of-disopyramide-and-new-medications-on-the-horizon-1100356.html" rel="noopener"><i class="fab fa-facebook-f"></i></a> <a class="nav-link" title="haga clic aqu铆" target="_blank" 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